Anti-pyruvate dehydrogenase (lipoamide) α 1 Monoclonal Antibody-抗体-抗体-生物在线
北京索莱宝科技有限公司
Anti-pyruvate dehydrogenase (lipoamide) α 1 Monoclonal Antibody

Anti-pyruvate dehydrogenase (lipoamide) α 1 Monoclonal Antibody

商家询价

产品名称: Anti-pyruvate dehydrogenase (lipoamide) α 1 Monoclonal Antibody

英文名称: Anti-pyruvate dehydrogenase (lipoamide) α 1 Monoclonal Antibody

产品编号: K001357M

产品价格: null

产品产地: 北京

品牌商标: solarbio

更新时间: 2025-11-20T09:58:30

使用范围: WB ICC

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Anti-pyruvate dehydrogenase (lipoamide) α 1 Monoclonal Antibody

品牌:solarbio | 货号:K001357M
商品货号:商品品牌:规格基本售价:选择规格
K001357M-50ulsolarbio50ul960.00元
K001357M-100ulsolarbio100ul1600.00元
英文名称Anti-pyruvate dehydrogenase (lipoamide) α 1 Monoclonal Antibody
别名PDHA;PDHAD;PDHCE1A;PHE1A
应用WB ICC
稀释比例WB 1:1000. IHC 1:100.
交叉反应Human Mouse
蛋白分子量43kDa
Gene ID5160
保存Store at -20°C. Avoid freeze / thaw cycles.
储存液Buffer: PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
纯化方法Affinity purification
亚型IgG1
免疫原Purified recombinant human Pyruvate Dehydrogenase protein fragments expressed in E.coli.
性状液体
Public Immunogen RangePurified recombinant human Pyruvate Dehydrogenase protein fragments expressed in E.coli.
Subcellular LocationsMitochondrion matrix
Swiss ProtP08559
克隆号3H2-F8-B5
克隆类型Monoclonal Antibody
背景资料The pyruvate dehydrogenase (PDH) complex is a nuclear-encoded mitochondrial multienzyme complex that catalyzes the overall conversion of pyruvate to acetyl-CoA and CO(2), and provides the primary link between glycolysis and the tricarboxylic acid (TCA) cycle. The PDH complex is composed of multiple copies of three enzymatic components: pyruvate dehydrogenase (E1), dihydrolipoamide acetyltransferase (E2) and lipoamide dehydrogenase (E3). The E1 enzyme is a heterotetramer of two alpha and two beta subunits. This gene encodes the E1 alpha 1 subunit containing the E1 active site, and plays a key role in the function of the PDH complex. Mutations in this gene are associated with pyruvate dehydrogenase E1-alpha deficiency and X-linked Leigh syndrome. Alternatively spliced transcript variants encoding different isoforms have been found for this gene.